{"id":108266,"date":"2011-06-05T00:00:00","date_gmt":"2011-06-05T00:00:00","guid":{"rendered":"https:\/\/www.deberes.net\/tesis\/sin-categoria\/valoracion-de-estado-de-salud-en-pacientes-con-porfiria\/"},"modified":"2011-06-05T00:00:00","modified_gmt":"2011-06-05T00:00:00","slug":"valoracion-de-estado-de-salud-en-pacientes-con-porfiria","status":"publish","type":"post","link":"https:\/\/www.deberes.net\/tesis\/ciencias-de-la-nutricion\/valoracion-de-estado-de-salud-en-pacientes-con-porfiria\/","title":{"rendered":"Valoraci\u00f3n de estado de salud en pacientes con porfiria."},"content":{"rendered":"<h2>Tesis doctoral de <strong> Jos\u00e9 Luis Gris Pi\u00f1ero <\/strong><\/h2>\n<p>La porfiria aguda intermitente (pai) es una enfermedad hereditaria rara, que supone un defecto cong\u00e9nito del metabolismo de las porfirinas de naturaleza enzim\u00e1tica. Una dieta equilibrada puede prevenir y\/o minimizar el n\u00famero y gravedad de los ataques y los s\u00edntomas de la enfermedad. Un tratamiento adecuado para la pai, es el incremento de carbohidratos en la dieta. el estudio se ha centrado en pacientes de porfiria aguda intermitente localizados en la regi\u00f3n de murcia, donde esta patolog\u00eda es end\u00e9mica. Los pacientes han sido evaluados a trav\u00e9s de cuestionarios nutricionales, biom\u00e9tricos y de calidad de vida (euroqol-5d, barthel y katz) , para describir su estatus nutricional evaluando su cumplimiento respecto a las recomendaciones nutricionales, nacionales e internacionales y compar\u00e1ndolos con controles sanos. Tambi\u00e9n se ha determinado su perfil enzim\u00e1tico antioxidante evaluando la actividad de enzimas antioxidantes (catalasa, super\u00f3xido dismutasa, glutati\u00f3n reductasa, glutati\u00f3n peroxidada y mieloperoxidasa) en eritrocitos, linfocitos, y neutr\u00f3filos. Todo ello dirigido al establecimiento de marcadores discriminantes de la patolog\u00eda que poseen. los resultados muestran que los pacientes llevan una dieta no equilibrada energ\u00e9tica y nutricionalmente por lo que los pacientes deber\u00edan ser monitorizados nutricionalmente para evitar posibles complicaciones y\/o signos de progresi\u00f3n. tambi\u00e9n se observa que son pacientes con alto grado de independencia y en la evaluaci\u00f3n de actividad de enzimas antioxidantes, s\u00f3lo la enzima super\u00f3xido dismutasa ser\u00eda un biomarcador de pacientes pai.<\/p>\n<p>&nbsp;<\/p>\n<h3>Datos acad\u00e9micos de la tesis doctoral \u00ab<strong>Valoraci\u00f3n de estado de salud en pacientes con porfiria.<\/strong>\u00ab<\/h3>\n<ul>\n<li><strong>T\u00edtulo de la tesis:<\/strong>\u00a0 Valoraci\u00f3n de estado de salud en pacientes con porfiria. <\/li>\n<li><strong>Autor:<\/strong>\u00a0 Jos\u00e9 Luis Gris Pi\u00f1ero <\/li>\n<li><strong>Universidad:<\/strong>\u00a0 Murcia<\/li>\n<li><strong>Fecha de lectura de la tesis:<\/strong>\u00a0 06\/05\/2011<\/li>\n<\/ul>\n<p>&nbsp;<\/p>\n<h3>Direcci\u00f3n y tribunal<\/h3>\n<ul>\n<li><strong>Director de la tesis<\/strong>\n<ul>\n<li>Antonia Mar\u00eda Jimenez Monreal<\/li>\n<\/ul>\n<\/li>\n<li><strong>Tribunal<\/strong>\n<ul>\n<li>Presidente del tribunal: Mar\u00eda  rosario fatima Olea serrano <\/li>\n<li>Miguel Mariscal arcas (vocal)<\/li>\n<li>sancho Jos\u00e9 Ba\u00f1on arias (vocal)<\/li>\n<li>Mar\u00eda Luisa Lorenzo tovar (vocal)<\/li>\n<\/ul>\n<\/li>\n<\/ul>\n<p>&nbsp;<\/p>\n","protected":false},"excerpt":{"rendered":"<p>Tesis doctoral de Jos\u00e9 Luis Gris Pi\u00f1ero La porfiria aguda intermitente (pai) es una enfermedad hereditaria rara, que supone un [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":0,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"site-sidebar-layout":"default","site-content-layout":"","ast-site-content-layout":"","site-content-style":"default","site-sidebar-style":"default","ast-global-header-display":"","ast-banner-title-visibility":"","ast-main-header-display":"","ast-hfb-above-header-display":"","ast-hfb-below-header-display":"","ast-hfb-mobile-header-display":"","site-post-title":"","ast-breadcrumbs-content":"","ast-featured-img":"","footer-sml-layout":"","theme-transparent-header-meta":"","adv-header-id-meta":"","stick-header-meta":"","header-above-stick-meta":"","header-main-stick-meta":"","header-below-stick-meta":"","astra-migrate-meta-layouts":"default","ast-page-background-enabled":"default","ast-page-background-meta":{"desktop":{"background-color":"var(--ast-global-color-4)","background-image":"","background-repeat":"repeat","background-position":"center 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