{"id":136729,"date":"2026-01-12T17:00:00","date_gmt":"2026-01-12T17:00:00","guid":{"rendered":"https:\/\/www.deberes.net\/tesis\/sin-categoria\/alteraciones-tubulares-en-la-poliquistosis-renal-hereditaria-del-adulto\/"},"modified":"2026-01-12T17:00:00","modified_gmt":"2026-01-12T17:00:00","slug":"alteraciones-tubulares-en-la-poliquistosis-renal-hereditaria-del-adulto","status":"publish","type":"post","link":"https:\/\/www.deberes.net\/tesis\/ciencias-medicas\/alteraciones-tubulares-en-la-poliquistosis-renal-hereditaria-del-adulto\/","title":{"rendered":"Alteraciones tubulares en la poliquistosis renal hereditaria del adulto"},"content":{"rendered":"<h2>Tesis doctoral de <strong>  Ruiz De Gauna Lopez De Heredia Ramon <\/strong><\/h2>\n<p>Se estudiaron diez y seis (16) pacientes con diagnostico de certeza de poliquistosis renal hereditaria del adulto encontrandose los siguientes hallazgos:  .Se comprobo indemnidad de las funciones tubulares proximales en el 100%  .Todos los pacientes (100%) acidificaban correctamente la orina (ph inferior a 5,5), pero en 5 pacientes (31%) existia un defecto en la amoniogenesis.  .La capacidad de concentracion estaba alterada en el 50% de los casos  .El 37% de los pacientes no presentaban ningun tipo de alteraciones en sus funciones tubulares tanto proximales como distales.  .Habitualmente, salvo un paciente, cuando existia alteracion en la amoniogenesis existia, asociado, un defecto en su capacidad de concentracion. Dicho paciente presentaba como unico defecto tubular una alteracion en la sintesis de amonio.  .Dado que existen pacientes sin alteraciones tubulares, no se puede emplear el estudio de las funciones tubulares como metodo diagnostico de esta entidad .En el estudio del funcionalismo tubular solo se han encontrado alteraciones de las funciones distales lo que no descarta que existan dilataciones proximales.<\/p>\n<p>&nbsp;<\/p>\n<h3>Datos acad\u00e9micos de la tesis doctoral \u00ab<strong>Alteraciones tubulares en la poliquistosis renal hereditaria del adulto<\/strong>\u00ab<\/h3>\n<ul>\n<li><strong>T\u00edtulo de la tesis:<\/strong>\u00a0 Alteraciones tubulares en la poliquistosis renal hereditaria del adulto <\/li>\n<li><strong>Autor:<\/strong>\u00a0  Ruiz De Gauna Lopez De Heredia Ramon <\/li>\n<li><strong>Universidad:<\/strong>\u00a0 Pa\u00eds vasco\/euskal herriko unibertsitatea<\/li>\n<li><strong>Fecha de lectura de la tesis:<\/strong>\u00a0 01\/01\/1991<\/li>\n<\/ul>\n<p>&nbsp;<\/p>\n<h3>Direcci\u00f3n y tribunal<\/h3>\n<ul>\n<li><strong>Director de la tesis<\/strong>\n<ul>\n<li>Juan Rodriguez Soriano<\/li>\n<\/ul>\n<\/li>\n<li><strong>Tribunal<\/strong>\n<ul>\n<li>Presidente del tribunal: Felipe Miguel De La Villa <\/li>\n<li> Arevalo Alonso Jos\u00e9 Miguel (vocal)<\/li>\n<li> Ortega Ruano Mar\u00eda  Rosa (vocal)<\/li>\n<li>Pedro Errasti Goenaga (vocal)<\/li>\n<\/ul>\n<\/li>\n<\/ul>\n<p>&nbsp;<\/p>\n","protected":false},"excerpt":{"rendered":"<p>Tesis doctoral de Ruiz De Gauna Lopez De Heredia Ramon Se estudiaron diez y seis (16) pacientes con diagnostico de [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":0,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"site-sidebar-layout":"default","site-content-layout":"","ast-site-content-layout":"","site-content-style":"default","site-sidebar-style":"default","ast-global-header-display":"","ast-banner-title-visibility":"","ast-main-header-display":"","ast-hfb-above-header-display":"","ast-hfb-below-header-display":"","ast-hfb-mobile-header-display":"","site-post-title":"","ast-breadcrumbs-content":"","ast-featured-img":"","footer-sml-layout":"","theme-transparent-header-meta":"","adv-header-id-meta":"","stick-header-meta":"","header-above-stick-meta":"","header-main-stick-meta":"","header-below-stick-meta":"","astra-migrate-meta-layouts":"default","ast-page-background-enabled":"default","ast-page-background-meta":{"desktop":{"background-color":"var(--ast-global-color-4)","background-image":"","background-repeat":"repeat","background-position":"center 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