{"id":138662,"date":"2026-01-12T17:37:28","date_gmt":"2026-01-12T17:37:28","guid":{"rendered":"https:\/\/www.deberes.net\/tesis\/sin-categoria\/estudio-del-modulo-del-factor-von-willebrand-para-su-union-al-fviii\/"},"modified":"2026-01-12T17:37:28","modified_gmt":"2026-01-12T17:37:28","slug":"estudio-del-modulo-del-factor-von-willebrand-para-su-union-al-fviii","status":"publish","type":"post","link":"https:\/\/www.deberes.net\/tesis\/ciencias-medicas\/estudio-del-modulo-del-factor-von-willebrand-para-su-union-al-fviii\/","title":{"rendered":"Estudio del modulo del factor von willebrand para su union al fviii"},"content":{"rendered":"<h2>Tesis doctoral de <strong>  Blanco Lopez M. Jose <\/strong><\/h2>\n<p>Se ha dise\u00f1ado un metodo sencillo, sensible y especifico capaz de detectar defectos de union total o parcial de fviii al factor von willebrand (fvw). Se describe una nueva familia con una patolog\u00eda selectiva del modulo funcional del fvw en su union al fviii con importantes implicaciones en la terapia, con una mala respuesta a concentrados de fviii y ddavp y buena respuesta a crioprecipitados, siendo los propositi homozigotos o doble heterozigotos y los restantes miembros heterozigotos para este defecto, demostrandose la existencia de una enfermedad de von willebrand (evw) con herencia de tipo autosomico recesivo.  contribuye al diagnostico de hemofilia a en una familia en la que se incluye a una mujer con hemofilia a.  se descarta la asociacion de la patolog\u00eda de este modulo con alteraciones estructurales multimericas al estudiar una familia con evw tipo id descrita en nuestro laboratorio.<\/p>\n<p>&nbsp;<\/p>\n<h3>Datos acad\u00e9micos de la tesis doctoral \u00ab<strong>Estudio del modulo del factor von willebrand para su union al fviii<\/strong>\u00ab<\/h3>\n<ul>\n<li><strong>T\u00edtulo de la tesis:<\/strong>\u00a0 Estudio del modulo del factor von willebrand para su union al fviii <\/li>\n<li><strong>Autor:<\/strong>\u00a0  Blanco Lopez M. Jose <\/li>\n<li><strong>Universidad:<\/strong>\u00a0 Santiago de compostela<\/li>\n<li><strong>Fecha de lectura de la tesis:<\/strong>\u00a0 01\/01\/1992<\/li>\n<\/ul>\n<p>&nbsp;<\/p>\n<h3>Direcci\u00f3n y tribunal<\/h3>\n<ul>\n<li><strong>Director de la tesis<\/strong>\n<ul>\n<li>Francisco Javier Batlle Fontrodona<\/li>\n<\/ul>\n<\/li>\n<li><strong>Tribunal<\/strong>\n<ul>\n<li>Presidente del tribunal: Carlos Acu\u00f1a Castroviejo <\/li>\n<li>Eduardo Rocha Hernando (vocal)<\/li>\n<li>Ricardo Castillo Cofi\u00f1o (vocal)<\/li>\n<li>Carlos Dieguez Gonzalez (vocal)<\/li>\n<\/ul>\n<\/li>\n<\/ul>\n<p>&nbsp;<\/p>\n","protected":false},"excerpt":{"rendered":"<p>Tesis doctoral de Blanco Lopez M. Jose Se ha dise\u00f1ado un metodo sencillo, sensible y especifico capaz de detectar defectos [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":0,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"site-sidebar-layout":"default","site-content-layout":"","ast-site-content-layout":"","site-content-style":"default","site-sidebar-style":"default","ast-global-header-display":"","ast-banner-title-visibility":"","ast-main-header-display":"","ast-hfb-above-header-display":"","ast-hfb-below-header-display":"","ast-hfb-mobile-header-display":"","site-post-title":"","ast-breadcrumbs-content":"","ast-featured-img":"","footer-sml-layout":"","theme-transparent-header-meta":"","adv-header-id-meta":"","stick-header-meta":"","header-above-stick-meta":"","header-main-stick-meta":"","header-below-stick-meta":"","astra-migrate-meta-layouts":"default","ast-page-background-enabled":"default","ast-page-background-meta":{"desktop":{"background-color":"var(--ast-global-color-4)","background-image":"","background-repeat":"repeat","background-position":"center center","background-size":"auto","background-attachment":"scroll","background-type":"","background-media":"","overlay-type":"","overlay-color":"","overlay-gradient":""},"tablet":{"background-color":"","background-image":"","background-repeat":"repeat","background-position":"center center","background-size":"auto","background-attachment":"scroll","background-type":"","background-media":"","overlay-type":"","overlay-color":"","overlay-gradient":""},"mobile":{"background-color":"","background-image":"","background-repeat":"repeat","background-position":"center center","background-size":"auto","background-attachment":"scroll","background-type":"","background-media":"","overlay-type":"","overlay-color":"","overlay-gradient":""}},"ast-content-background-meta":{"desktop":{"background-color":"var(--ast-global-color-5)","background-image":"","background-repeat":"repeat","background-position":"center center","background-size":"auto","background-attachment":"scroll","background-type":"","background-media":"","overlay-type":"","overlay-color":"","overlay-gradient":""},"tablet":{"background-color":"var(--ast-global-color-5)","background-image":"","background-repeat":"repeat","background-position":"center center","background-size":"auto","background-attachment":"scroll","background-type":"","background-media":"","overlay-type":"","overlay-color":"","overlay-gradient":""},"mobile":{"background-color":"var(--ast-global-color-5)","background-image":"","background-repeat":"repeat","background-position":"center center","background-size":"auto","background-attachment":"scroll","background-type":"","background-media":"","overlay-type":"","overlay-color":"","overlay-gradient":""}},"footnotes":""},"categories":[9,218,139,156,977,12395],"tags":[253188,41973,15487,8788,9708,198],"class_list":["post-138662","post","type-post","status-publish","format-standard","hentry","category-ciencias-medicas","category-hematologia","category-medicina-interna","category-patologia","category-santiago-de-compostela","category-trombosis","tag-blanco-lopez-m-jose","tag-carlos-acuna-castroviejo","tag-carlos-dieguez-gonzalez","tag-eduardo-rocha-hernando","tag-francisco-javier-batlle-fontrodona","tag-ricardo-castillo-cofino"],"_links":{"self":[{"href":"https:\/\/www.deberes.net\/tesis\/wp-json\/wp\/v2\/posts\/138662","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/www.deberes.net\/tesis\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/www.deberes.net\/tesis\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/www.deberes.net\/tesis\/wp-json\/wp\/v2\/users\/1"}],"replies":[{"embeddable":true,"href":"https:\/\/www.deberes.net\/tesis\/wp-json\/wp\/v2\/comments?post=138662"}],"version-history":[{"count":0,"href":"https:\/\/www.deberes.net\/tesis\/wp-json\/wp\/v2\/posts\/138662\/revisions"}],"wp:attachment":[{"href":"https:\/\/www.deberes.net\/tesis\/wp-json\/wp\/v2\/media?parent=138662"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/www.deberes.net\/tesis\/wp-json\/wp\/v2\/categories?post=138662"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/www.deberes.net\/tesis\/wp-json\/wp\/v2\/tags?post=138662"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}