{"id":139231,"date":"2026-01-12T17:43:15","date_gmt":"2026-01-12T17:43:15","guid":{"rendered":"https:\/\/www.deberes.net\/tesis\/sin-categoria\/la-esferocitosis-hereditaria-y-su-diagnostico-en-la-practica-clinica\/"},"modified":"2026-01-12T17:43:15","modified_gmt":"2026-01-12T17:43:15","slug":"la-esferocitosis-hereditaria-y-su-diagnostico-en-la-practica-clinica","status":"publish","type":"post","link":"https:\/\/www.deberes.net\/tesis\/ciencias-medicas\/la-esferocitosis-hereditaria-y-su-diagnostico-en-la-practica-clinica\/","title":{"rendered":"La esferocitosis hereditaria y su diagnostico en la practica clinica"},"content":{"rendered":"<h2>Tesis doctoral de <strong>  Ricard Andr\u00e9s M. Pilar <\/strong><\/h2>\n<p>Nuestro estudio de 62 enfermos de esferocitosis hereditaria (eh) (19 esplenectomizados) y 6 parejas progenitoras de casos sin historia familiar ha confirmado la habitual herencia dominante y diversidad clinica del problema. Hemos demostrado que la citometria de difraccion de luz laser es un metodo util, preciso, rapido y muy eficaz para la deteccion objetiva de la esferocitosis, que cuantifica proporcionalmente a la gravedad de la entidad, merced a los parametros hc, area ii y % hiper. Como indicadores de esferocitosis, estas variables superan a la fragilidad asmatica y tecnicas relacionadas, a las que pueda reemplazar en el diagnostico de la eh. Pero para ello, la demostracion de esferocitosis ha de formar parte de un conjunto de datos clinicos y biologicos propios de eh. La sds-page de las membranas eritrocitarias aisladas es un metodo sencillo, eficaz y reproducible para la estimacion de los contenidos de espectrina y ankirina. Ha permitido constatar el deficit parcial de espectrina proporcional a la gravedad de la eh.<\/p>\n<p>&nbsp;<\/p>\n<h3>Datos acad\u00e9micos de la tesis doctoral \u00ab<strong>La esferocitosis hereditaria y su diagnostico en la practica clinica<\/strong>\u00ab<\/h3>\n<ul>\n<li><strong>T\u00edtulo de la tesis:<\/strong>\u00a0 La esferocitosis hereditaria y su diagnostico en la practica clinica <\/li>\n<li><strong>Autor:<\/strong>\u00a0  Ricard Andr\u00e9s M. Pilar <\/li>\n<li><strong>Universidad:<\/strong>\u00a0 Complutense de Madrid<\/li>\n<li><strong>Fecha de lectura de la tesis:<\/strong>\u00a0 01\/01\/1992<\/li>\n<\/ul>\n<p>&nbsp;<\/p>\n<h3>Direcci\u00f3n y tribunal<\/h3>\n<ul>\n<li><strong>Director de la tesis<\/strong>\n<ul>\n<li>Florinda Gilsanz Rodriguez<\/li>\n<\/ul>\n<\/li>\n<li><strong>Tribunal<\/strong>\n<ul>\n<li>Presidente del tribunal: Dominga Espinos Perez <\/li>\n<li>Angel Nogales Espert (vocal)<\/li>\n<li>Jos\u00e9 Sanchez Fayos (vocal)<\/li>\n<li> Barbolla Garcia M. Luz (vocal)<\/li>\n<\/ul>\n<\/li>\n<\/ul>\n<p>&nbsp;<\/p>\n","protected":false},"excerpt":{"rendered":"<p>Tesis doctoral de Ricard Andr\u00e9s M. Pilar Nuestro estudio de 62 enfermos de esferocitosis hereditaria (eh) (19 esplenectomizados) y 6 [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":0,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"site-sidebar-layout":"default","site-content-layout":"","ast-site-content-layout":"","site-content-style":"default","site-sidebar-style":"default","ast-global-header-display":"","ast-banner-title-visibility":"","ast-main-header-display":"","ast-hfb-above-header-display":"","ast-hfb-below-header-display":"","ast-hfb-mobile-header-display":"","site-post-title":"","ast-breadcrumbs-content":"","ast-featured-img":"","footer-sml-layout":"","theme-transparent-header-meta":"","adv-header-id-meta":"","stick-header-meta":"","header-above-stick-meta":"","header-main-stick-meta":"","header-below-stick-meta":"","astra-migrate-meta-layouts":"default","ast-page-background-enabled":"default","ast-page-background-meta":{"desktop":{"background-color":"var(--ast-global-color-4)","background-image":"","background-repeat":"repeat","background-position":"center center","background-size":"auto","background-attachment":"scroll","background-type":"","background-media":"","overlay-type":"","overlay-color":"","overlay-gradient":""},"tablet":{"background-color":"","background-image":"","background-repeat":"repeat","background-position":"center center","background-size":"auto","background-attachment":"scroll","background-type":"","background-media":"","overlay-type":"","overlay-color":"","overlay-gradient":""},"mobile":{"background-color":"","background-image":"","background-repeat":"repeat","background-position":"center center","background-size":"auto","background-attachment":"scroll","background-type":"","background-media":"","overlay-type":"","overlay-color":"","overlay-gradient":""}},"ast-content-background-meta":{"desktop":{"background-color":"var(--ast-global-color-5)","background-image":"","background-repeat":"repeat","background-position":"center center","background-size":"auto","background-attachment":"scroll","background-type":"","background-media":"","overlay-type":"","overlay-color":"","overlay-gradient":""},"tablet":{"background-color":"var(--ast-global-color-5)","background-image":"","background-repeat":"repeat","background-position":"center center","background-size":"auto","background-attachment":"scroll","background-type":"","background-media":"","overlay-type":"","overlay-color":"","overlay-gradient":""},"mobile":{"background-color":"var(--ast-global-color-5)","background-image":"","background-repeat":"repeat","background-position":"center center","background-size":"auto","background-attachment":"scroll","background-type":"","background-media":"","overlay-type":"","overlay-color":"","overlay-gradient":""}},"footnotes":""},"categories":[9,986,218,139],"tags":[7781,176424,253756,30150,30138,253755],"class_list":["post-139231","post","type-post","status-publish","format-standard","hentry","category-ciencias-medicas","category-complutense-de-madrid","category-hematologia","category-medicina-interna","tag-angel-nogales-espert","tag-barbolla-garcia-m-luz","tag-dominga-espinos-perez","tag-florinda-gilsanz-rodriguez","tag-jose-sanchez-fayos","tag-ricard-andres-m-pilar"],"_links":{"self":[{"href":"https:\/\/www.deberes.net\/tesis\/wp-json\/wp\/v2\/posts\/139231","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/www.deberes.net\/tesis\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/www.deberes.net\/tesis\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/www.deberes.net\/tesis\/wp-json\/wp\/v2\/users\/1"}],"replies":[{"embeddable":true,"href":"https:\/\/www.deberes.net\/tesis\/wp-json\/wp\/v2\/comments?post=139231"}],"version-history":[{"count":0,"href":"https:\/\/www.deberes.net\/tesis\/wp-json\/wp\/v2\/posts\/139231\/revisions"}],"wp:attachment":[{"href":"https:\/\/www.deberes.net\/tesis\/wp-json\/wp\/v2\/media?parent=139231"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/www.deberes.net\/tesis\/wp-json\/wp\/v2\/categories?post=139231"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/www.deberes.net\/tesis\/wp-json\/wp\/v2\/tags?post=139231"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}