{"id":156149,"date":"2026-01-12T17:26:37","date_gmt":"2026-01-12T17:26:37","guid":{"rendered":"https:\/\/www.deberes.net\/tesis\/sin-categoria\/la-epilepsia-mioclonica-juvenil-caracteristicas-clinicas-y-neuro-fisiologicas\/"},"modified":"2026-01-12T17:26:37","modified_gmt":"2026-01-12T17:26:37","slug":"la-epilepsia-mioclonica-juvenil-caracteristicas-clinicas-y-neuro-fisiologicas","status":"publish","type":"post","link":"https:\/\/www.deberes.net\/tesis\/ciencias-medicas\/la-epilepsia-mioclonica-juvenil-caracteristicas-clinicas-y-neuro-fisiologicas\/","title":{"rendered":"La epilepsia mioclonica juvenil: caracteristicas clinicas y neuro-fisiologicas"},"content":{"rendered":"<h2>Tesis doctoral de <strong> Javier Salas Puig <\/strong><\/h2>\n<p>Se estudiaron 50 pacientes, afectos de epilepsia mioclonica juvenil (emj), con protocolo prospectivo, que incluia: historia clinica, electroencefalograma (eeg) de vigilia, poligrafia de sue\u00f1o y potenciales evocados visuales (pev), auditivos de tronco cerebral (peatc) y somatosensoriales (pess). Los datos obtenidos se han comparado con los de otros grupos de epilepsia generalizada primaria (egp), ausencias o gran mal, de similar edad y tiempo de seguimiento. La emj es un sindrome epileptico bien individualizado, que se caracteriza por: 1) antecedentes familiares de epilepsia en alto indice, mioclonias sobre todo del despertar con estados mioclonicos en la evolucion, buena respuesta al tratamiento con valproato y alto porcentaje de recaidas.  2) eeg en vigilia: normal o con poli-punta onda generalizada y frecuente respuesta fotoconvulsiva favorecida por el cierre palpebral. En sue\u00f1o nrem:  aumento constante de los paroxismos. 3) pess de latencia normal pero mayor amplitud (a veces \u00abgigantes\u00bb) que en otras egp. Peatc con intervalo i-v alargado en relacion con farmacos antipilepticos y no con la epilepsia. Pev normales, aun en aquellos que presentaban respuesta fotoparoxistica en el eeg tras estimulacion luminosa intermitente.<\/p>\n<p>&nbsp;<\/p>\n<h3>Datos acad\u00e9micos de la tesis doctoral \u00ab<strong>La epilepsia mioclonica juvenil: caracteristicas clinicas y neuro-fisiologicas<\/strong>\u00ab<\/h3>\n<ul>\n<li><strong>T\u00edtulo de la tesis:<\/strong>\u00a0 La epilepsia mioclonica juvenil: caracteristicas clinicas y neuro-fisiologicas <\/li>\n<li><strong>Autor:<\/strong>\u00a0 Javier Salas Puig <\/li>\n<li><strong>Universidad:<\/strong>\u00a0 Oviedo<\/li>\n<li><strong>Fecha de lectura de la tesis:<\/strong>\u00a0 01\/01\/1991<\/li>\n<\/ul>\n<p>&nbsp;<\/p>\n<h3>Direcci\u00f3n y tribunal<\/h3>\n<ul>\n<li><strong>Director de la tesis<\/strong>\n<ul>\n<li>Jos\u00e9 Ignacio Fernandez Bernaldo De Quiros<\/li>\n<\/ul>\n<\/li>\n<li><strong>Tribunal<\/strong>\n<ul>\n<li>Presidente del tribunal: Eduardo Tolosa Sarr\u00f3 <\/li>\n<li>Bernardino Blazquez Menes (vocal)<\/li>\n<li>Jos\u00e9 Luis Herranz Fernandez (vocal)<\/li>\n<li>Francisco Morales Asin (vocal)<\/li>\n<\/ul>\n<\/li>\n<\/ul>\n<p>&nbsp;<\/p>\n","protected":false},"excerpt":{"rendered":"<p>Tesis doctoral de Javier Salas Puig Se estudiaron 50 pacientes, afectos de epilepsia mioclonica juvenil (emj), con protocolo prospectivo, que 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