{"id":17889,"date":"2018-03-09T09:06:11","date_gmt":"2018-03-09T09:06:11","guid":{"rendered":"https:\/\/www.deberes.net\/tesis\/sin-categoria\/aproximacion-al-tratamiento-integral-del-sindrome-de-wolfram\/"},"modified":"2018-03-09T09:06:11","modified_gmt":"2018-03-09T09:06:11","slug":"aproximacion-al-tratamiento-integral-del-sindrome-de-wolfram","status":"publish","type":"post","link":"https:\/\/www.deberes.net\/tesis\/ciencias-medicas\/aproximacion-al-tratamiento-integral-del-sindrome-de-wolfram\/","title":{"rendered":"Aproximaci\u00f3n al tratamiento integral del sindrome de wolfram"},"content":{"rendered":"<h2>Tesis doctoral de <strong> Gema Esteban Bueno <\/strong><\/h2>\n<p>El sindrome de wolfram (didmoad) es una entidad compleja, hereditaria de muy baja preValencia. Basicamente esta constituida por la asociaci\u00f3n de diabetes mellitus y atr\u00f3fia \u00f3ptica, concurren en frecuencia variables otras entidades, siendo las m\u00e1s frecuentes diabetes ins\u00edpida, &#8212; y alteraciones de la v\u00eda urinaria.  la serie de pacientes recogidas en nuestro trabajo (n=23) representa el mayor conjunto de pacientes con s\u00edndrome de wolfram diagn\u00f3sticados en nuestro pa\u00eds. Se aporta una visi\u00f3n biopsico social acerca de la problem\u00e1tica de estos enfermos:  * se ha realizado una amplia recopilaci\u00f3n de informaci\u00f3n acerca de esta patolog\u00eda y hasta el momento actual estaba muy dispersa.  * se comentan las caracter\u00edsticas cl\u00ednicas de nuestros parientes compar\u00e1ndolos con las series m\u00e1s amplios previamente publicados, haciendose especial hincapi\u00e9 en la diferencia de edad a la que aparecen los s\u00edntomas y el momento del diagn\u00f3stico cl\u00ednico que cada uno de los s\u00edntomas comporta.  * se realiza una valoraci\u00f3n de como este s\u00edndrome &#8212; la calidad de vida de los enfermos y sus familiares para lo que se ha utilizado el c.C.V., y la manera de afrontar la enfermedad por ambos.  * se hace una valoraci\u00f3n de los s\u00edntomas que afecta m\u00e1s en calidad de vida.  * se valora la importancia de la creaci\u00f3n de un \u00abgrupo de apoyo\u00bb para ellos.<\/p>\n<p>&nbsp;<\/p>\n<h3>Datos acad\u00e9micos de la tesis doctoral \u00ab<strong>Aproximaci\u00f3n al tratamiento integral del sindrome de wolfram<\/strong>\u00ab<\/h3>\n<ul>\n<li><strong>T\u00edtulo de la tesis:<\/strong>\u00a0 Aproximaci\u00f3n al tratamiento integral del sindrome de wolfram <\/li>\n<li><strong>Autor:<\/strong>\u00a0 Gema Esteban Bueno <\/li>\n<li><strong>Universidad:<\/strong>\u00a0 Sevilla<\/li>\n<li><strong>Fecha de lectura de la tesis:<\/strong>\u00a0 28\/06\/2002<\/li>\n<\/ul>\n<p>&nbsp;<\/p>\n<h3>Direcci\u00f3n y tribunal<\/h3>\n<ul>\n<li><strong>Director de la tesis<\/strong>\n<ul>\n<li>Santiago Dur\u00e1n Garc\u00eda<\/li>\n<\/ul>\n<\/li>\n<li><strong>Tribunal<\/strong>\n<ul>\n<li>Presidente del tribunal: \u00e1ngel Mara\u00f1\u00f3n cabello <\/li>\n<li>mercedes Rodr\u00edguez rigual (vocal)<\/li>\n<li>Jos\u00e9 Gonz\u00e1lez machero (vocal)<\/li>\n<li>Javier Dapena Francisco (vocal)<\/li>\n<\/ul>\n<\/li>\n<\/ul>\n<p>&nbsp;<\/p>\n","protected":false},"excerpt":{"rendered":"<p>Tesis doctoral de Gema Esteban Bueno El sindrome de wolfram (didmoad) es una entidad compleja, hereditaria de muy baja preValencia. [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":0,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"site-sidebar-layout":"default","site-content-layout":"","ast-site-content-layout":"","site-content-style":"default","site-sidebar-style":"default","ast-global-header-display":"","ast-banner-title-visibility":"","ast-main-header-display":"","ast-hfb-above-header-display":"","ast-hfb-below-header-display":"","ast-hfb-mobile-header-display":"","site-post-title":"","ast-breadcrumbs-content":"","ast-featured-img":"","footer-sml-layout":"","theme-transparent-header-meta":"","adv-header-id-meta":"","stick-header-meta":"","header-above-stick-meta":"","header-main-stick-meta":"","header-below-stick-meta":"","astra-migrate-meta-layouts":"default","ast-page-background-enabled":"default","ast-page-background-meta":{"desktop":{"background-color":"var(--ast-global-color-4)","background-image":"","background-repeat":"repeat","background-position":"center center","background-size":"auto","background-attachment":"scroll","background-type":"","background-media":"","overlay-type":"","overlay-color":"","overlay-gradient":""},"tablet":{"background-color":"","background-image":"","background-repeat":"repeat","background-position":"center center","background-size":"auto","background-attachment":"scroll","background-type":"","background-media":"","overlay-type":"","overlay-color":"","overlay-gradient":""},"mobile":{"background-color":"","background-image":"","background-repeat":"repeat","background-position":"center center","background-size":"auto","background-attachment":"scroll","background-type":"","background-media":"","overlay-type":"","overlay-color":"","overlay-gradient":""}},"ast-content-background-meta":{"desktop":{"background-color":"var(--ast-global-color-5)","background-image":"","background-repeat":"repeat","background-position":"center center","background-size":"auto","background-attachment":"scroll","background-type":"","background-media":"","overlay-type":"","overlay-color":"","overlay-gradient":""},"tablet":{"background-color":"var(--ast-global-color-5)","background-image":"","background-repeat":"repeat","background-position":"center center","background-size":"auto","background-attachment":"scroll","background-type":"","background-media":"","overlay-type":"","overlay-color":"","overlay-gradient":""},"mobile":{"background-color":"var(--ast-global-color-5)","background-image":"","background-repeat":"repeat","background-position":"center center","background-size":"auto","background-attachment":"scroll","background-type":"","background-media":"","overlay-type":"","overlay-color":"","overlay-gradient":""}},"footnotes":""},"categories":[155,35,9,962,11771,1820,161,324,996,10715],"tags":[27683,55759,55761,10875,55760,19602],"class_list":["post-17889","post","type-post","status-publish","format-standard","hentry","category-ciencias-clinicas","category-ciencias-de-la-vida","category-ciencias-medicas","category-genetica","category-genetica-clinica","category-genetica-de-poblaciones","category-pediatria","category-psicologia","category-psicologia-social","category-sevilla","tag-angel-maranon-cabello","tag-gema-esteban-bueno","tag-javier-dapena-francisco","tag-jose-gonzalez-machero","tag-mercedes-rodriguez-rigual","tag-santiago-duran-garcia"],"_links":{"self":[{"href":"https:\/\/www.deberes.net\/tesis\/wp-json\/wp\/v2\/posts\/17889","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/www.deberes.net\/tesis\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/www.deberes.net\/tesis\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/www.deberes.net\/tesis\/wp-json\/wp\/v2\/users\/1"}],"replies":[{"embeddable":true,"href":"https:\/\/www.deberes.net\/tesis\/wp-json\/wp\/v2\/comments?post=17889"}],"version-history":[{"count":0,"href":"https:\/\/www.deberes.net\/tesis\/wp-json\/wp\/v2\/posts\/17889\/revisions"}],"wp:attachment":[{"href":"https:\/\/www.deberes.net\/tesis\/wp-json\/wp\/v2\/media?parent=17889"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/www.deberes.net\/tesis\/wp-json\/wp\/v2\/categories?post=17889"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/www.deberes.net\/tesis\/wp-json\/wp\/v2\/tags?post=17889"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}