{"id":26603,"date":"2018-03-09T09:18:30","date_gmt":"2018-03-09T09:18:30","guid":{"rendered":"https:\/\/www.deberes.net\/tesis\/sin-categoria\/evolucion-de-los-hallazgos-ecocardiograficos-de-la-miocardiopata%c2%ada-hipertrofica-relacion-con-factores-de-riesgo-de-muerte-subita\/"},"modified":"2018-03-09T09:18:30","modified_gmt":"2018-03-09T09:18:30","slug":"evolucion-de-los-hallazgos-ecocardiograficos-de-la-miocardiopata%c2%ada-hipertrofica-relacion-con-factores-de-riesgo-de-muerte-subita","status":"publish","type":"post","link":"https:\/\/www.deberes.net\/tesis\/murcia\/evolucion-de-los-hallazgos-ecocardiograficos-de-la-miocardiopata%c2%ada-hipertrofica-relacion-con-factores-de-riesgo-de-muerte-subita\/","title":{"rendered":"Evoluci\u00f3n de los hallazgos ecocardiogr\u00e1ficos de la miocardiopat\u00edahipertr\u00f3fica. relaci\u00f3n con factores de riesgo de muerte s\u00fabita."},"content":{"rendered":"<h2>Tesis doctoral de <strong> Juan  Ramon Gimeno Blanes <\/strong><\/h2>\n<p>Introducci\u00f3n  la miocardipat\u00eda hipertr\u00f3fica (mh) es una enfermedad primaria del miocardio producida por mutaciones en genes que codifican prote\u00ednas del sarc\u00f3mero. desde el punto de vista anatomopatol\u00f3gico, la mh se caracteriza por la presencia de hipertrofia mioc\u00e1rdica, desorganizaci\u00f3n de los miocitos (\u00abdisarray\u00bb) y fibrosis que contribuyen al desarrollo de un amplio espectro de anomal\u00edas funcionales, incluyendo isquemia mioc\u00e1rdica, disfunci\u00f3n diast\u00f3lica, insuficiencia cardiaca congestiva, arritmias y muerte s\u00fabita.  es una condici\u00f3n que afecta entre un 1\/100 y un 1\/1000 de la poblaci\u00f3n. el desarrollo de hipertrofia mioc\u00e1rdica coincide con la fase de crecimiento, pudiendo observarse los grados m\u00e1s floridos en la adolescencia y juventud.  la mayor\u00eda de los afectados son asintom\u00e1ticos y los diagn\u00f3sticos se producen de forma casual o tras un estudio familiar. La sintomatolog\u00eda de esta enfermedad es variable y m\u00e1s frecuente, aunque no exclusiva, en las formas obstructivas. la muerte s\u00fabita, es la primera causa de fallecimiento entre los pacientes afectados de esta enfermedad. Un porcentaje menor de pacientes desarrolla disfunci\u00f3n y dilataci\u00f3n ventricular izquierda de la que se deriva la muerte o el trasplante por fallo cardiaco.  habitualmente, se suele apreciar hipertrofia ventricular en la ecograf\u00eda, siendo la caracter\u00edstica diagn\u00f3stica fundamental. En un porcentaje importante (25%), es posible identificar gradiente sist\u00f3lico din\u00e1mico en el tracto de salida del ventr\u00edculo izquierdo.  a pesar de lso continuos esfuerzos realizados en la investigaci\u00f3n de esta enfermedad, existen m\u00faltiples aspectos controvertidos relacionados con su manejo cl\u00ednico, siendo el principal la identificaci\u00f3n y tratamiento de los pacientes con alto riesgo de muerte s\u00fabita. La muerte s\u00fabita puede producirse a cualquier edad con una incidencia anual de un 1-4%.La mayor\u00eda de las muertes s\u00fabitas se producen en la adolescencia.<\/p>\n<p>&nbsp;<\/p>\n<h3>Datos acad\u00e9micos de la tesis doctoral \u00ab<strong>Evoluci\u00f3n de los hallazgos ecocardiogr\u00e1ficos de la miocardiopat\u00edahipertr\u00f3fica. relaci\u00f3n con factores de riesgo de muerte s\u00fabita.<\/strong>\u00ab<\/h3>\n<ul>\n<li><strong>T\u00edtulo de la tesis:<\/strong>\u00a0 Evoluci\u00f3n de los hallazgos ecocardiogr\u00e1ficos de la miocardiopat\u00edahipertr\u00f3fica. relaci\u00f3n con factores de riesgo de muerte s\u00fabita. <\/li>\n<li><strong>Autor:<\/strong>\u00a0 Juan  Ramon Gimeno Blanes <\/li>\n<li><strong>Universidad:<\/strong>\u00a0 Murcia<\/li>\n<li><strong>Fecha de lectura de la tesis:<\/strong>\u00a0 31\/10\/2003<\/li>\n<\/ul>\n<p>&nbsp;<\/p>\n<h3>Direcci\u00f3n y tribunal<\/h3>\n<ul>\n<li><strong>Director de la tesis<\/strong>\n<ul>\n<li>John Mckenna William<\/li>\n<\/ul>\n<\/li>\n<li><strong>Tribunal<\/strong>\n<ul>\n<li>Presidente del tribunal: alfonso Castro beiras <\/li>\n<li>Fernando Alfonso manterola (vocal)<\/li>\n<li>Manuel Penas lado (vocal)<\/li>\n<li> De la morena valenzuela gonzalo (vocal)<\/li>\n<\/ul>\n<\/li>\n<\/ul>\n<p>&nbsp;<\/p>\n","protected":false},"excerpt":{"rendered":"<p>Tesis doctoral de Juan Ramon Gimeno Blanes Introducci\u00f3n la miocardipat\u00eda hipertr\u00f3fica (mh) es una enfermedad primaria del miocardio producida por [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":0,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"site-sidebar-layout":"default","site-content-layout":"","ast-site-content-layout":"","site-content-style":"default","site-sidebar-style":"default","ast-global-header-display":"","ast-banner-title-visibility":"","ast-main-header-display":"","ast-hfb-above-header-display":"","ast-hfb-below-header-display":"","ast-hfb-mobile-header-display":"","site-post-title":"","ast-breadcrumbs-content":"","ast-featured-img":"","footer-sml-layout":"","theme-transparent-header-meta":"","adv-header-id-meta":"","stick-header-meta":"","header-above-stick-meta":"","header-main-stick-meta":"","header-below-stick-meta":"","astra-migrate-meta-layouts":"default","ast-page-background-enabled":"default","ast-page-background-meta":{"desktop":{"background-color":"var(--ast-global-color-4)","background-image":"","background-repeat":"repeat","background-position":"center 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