{"id":75968,"date":"2018-03-09T23:21:19","date_gmt":"2018-03-09T23:21:19","guid":{"rendered":"https:\/\/www.deberes.net\/tesis\/sin-categoria\/profilaxis-en-hemofilia-experiencia-en-aragon\/"},"modified":"2018-03-09T23:21:19","modified_gmt":"2018-03-09T23:21:19","slug":"profilaxis-en-hemofilia-experiencia-en-aragon","status":"publish","type":"post","link":"https:\/\/www.deberes.net\/tesis\/hematologia\/profilaxis-en-hemofilia-experiencia-en-aragon\/","title":{"rendered":"Profilaxis en hemofilia: experiencia en arag\u00f3n."},"content":{"rendered":"<h2>Tesis doctoral de <strong> Manuela Dob\u00f3n Rebollo <\/strong><\/h2>\n<p>Los avances logrados en las \u00faltimas d\u00e9cadas en el tratamiento de la hemofilia han conseguido cambiar el curso natural de la enfermedad.  La prevenci\u00f3n de la artropat\u00eda hemof\u00edlica ha constituido el objetivo principal del tratamiento en hemofilia.   el objetivo de nuestro estudio ha sido analizar la experiencia del programa de profilaxis que el hospital universitario miguel servet ha llevado a cabo en hemof\u00edlicos de arag\u00f3n, desde su inicio en el a\u00f1o 1992 hasta el 31-12-2003, as\u00ed como el per\u00edodo de tiempo en que dichos pacientes recibieron tratamiento a demanda.  Se trata de un estudio observacional, descriptivo y anal\u00edtico, con la recogida de datos de tipo demogr\u00e1fico y de tipo m\u00e9dico de las siguientes poblaciones: a) pacientes hemof\u00edlicos vivos de arag\u00f3n (a fecha 31-12-2003); b) pacientes hemof\u00edlicos de arag\u00f3n cuyas edades estaban comprendidas entre los 0 y 18 a\u00f1os (a fecha 31-12-2003); y c) pacientes hemof\u00edlicos de arag\u00f3n que segu\u00edan (a fecha 31-12-2003) un programa de profilaxis. El tiempo total de seguimiento durante el tratamiento a demanda fue 60,4 a\u00f1os con una media de 3,8 a\u00f1os y el tiempo total de seguimiento durante profilaxis fue 85,3 a\u00f1os con una media de 5,3 a\u00f1os. tras el an\u00e1lisis de los resultados se obtuvieron las siguientes conclusiones: 1) desde la puesta en marcha del programa de profilaxis en nuestra comunidad en el a\u00f1o 1992  hasta el 31-12-2003, el n\u00famero de hemof\u00edlicos menores de 18 a\u00f1os de edad inclu\u00eddos ha sido 16 pacientes. Recib\u00edan profilaxis el 88,2% del total de hemof\u00edlicos graves de este grupo de edad. De ellos, 14 padec\u00edan hemofilia a y 2 hemofilia b.  El grado de enfermedad m\u00e1s frecuente fue el grave en 15 casos y leve en 1 caso. 2) el tipo de profilaxis m\u00e1s frecuentemente administrada ha sido la profilaxis secundaria, seguida de la profilaxis primaria y de la de corta duraci\u00f3n. 3) tras iniciar profilaxis, se produjo un incremento estad\u00edsticamente significativo del consumo de factor, pasando de una m<\/p>\n<p>&nbsp;<\/p>\n<h3>Datos acad\u00e9micos de la tesis doctoral \u00ab<strong>Profilaxis en hemofilia: experiencia en arag\u00f3n.<\/strong>\u00ab<\/h3>\n<ul>\n<li><strong>T\u00edtulo de la tesis:<\/strong>\u00a0 Profilaxis en hemofilia: experiencia en arag\u00f3n. <\/li>\n<li><strong>Autor:<\/strong>\u00a0 Manuela Dob\u00f3n Rebollo <\/li>\n<li><strong>Universidad:<\/strong>\u00a0 Zaragoza<\/li>\n<li><strong>Fecha de lectura de la tesis:<\/strong>\u00a0 22\/07\/2005<\/li>\n<\/ul>\n<p>&nbsp;<\/p>\n<h3>Direcci\u00f3n y tribunal<\/h3>\n<ul>\n<li><strong>Director de la tesis<\/strong>\n<ul>\n<li>Martin Gutierrez Martin<\/li>\n<\/ul>\n<\/li>\n<li><strong>Tribunal<\/strong>\n<ul>\n<li>Presidente del tribunal: felipe Querol fuentes <\/li>\n<li>plar Rabasa baraibar (vocal)<\/li>\n<li>Manuel Giralt raichs (vocal)<\/li>\n<li>rosa Cornudella lacasa (vocal)<\/li>\n<\/ul>\n<\/li>\n<\/ul>\n<p>&nbsp;<\/p>\n","protected":false},"excerpt":{"rendered":"<p>Tesis doctoral de Manuela Dob\u00f3n Rebollo Los avances logrados en las \u00faltimas d\u00e9cadas en el tratamiento de la hemofilia han [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":0,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"site-sidebar-layout":"default","site-content-layout":"","ast-site-content-layout":"","site-content-style":"default","site-sidebar-style":"default","ast-global-header-display":"","ast-banner-title-visibility":"","ast-main-header-display":"","ast-hfb-above-header-display":"","ast-hfb-below-header-display":"","ast-hfb-mobile-header-display":"","site-post-title":"","ast-breadcrumbs-content":"","ast-featured-img":"","footer-sml-layout":"","theme-transparent-header-meta":"","adv-header-id-meta":"","stick-header-meta":"","header-above-stick-meta":"","header-main-stick-meta":"","header-below-stick-meta":"","astra-migrate-meta-layouts":"default","ast-page-background-enabled":"default","ast-page-background-meta":{"desktop":{"background-color":"var(--ast-global-color-4)","background-image":"","background-repeat":"repeat","background-position":"center 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