{"id":90115,"date":"2001-11-05T00:00:00","date_gmt":"2001-11-05T00:00:00","guid":{"rendered":"https:\/\/www.deberes.net\/tesis\/sin-categoria\/perfil-neuropsicologico-de-las-ataxias-cerebelosas-heredodegenerativas\/"},"modified":"2001-11-05T00:00:00","modified_gmt":"2001-11-05T00:00:00","slug":"perfil-neuropsicologico-de-las-ataxias-cerebelosas-heredodegenerativas","status":"publish","type":"post","link":"https:\/\/www.deberes.net\/tesis\/psicologia\/perfil-neuropsicologico-de-las-ataxias-cerebelosas-heredodegenerativas\/","title":{"rendered":"Perfil neuropsicologico de las ataxias cerebelosas heredodegenerativas"},"content":{"rendered":"<h2>Tesis doctoral de <strong> Tone Wollmann Engeby <\/strong><\/h2>\n<p>Este trabajo de investigaci\u00f3n valora el perfil neuropsicologico que caracteriza a una uestra de pacientes con ataxia cerebelosa heredodegenerativa. se trata de pacientes que cumplen criterios clinicos de ataxia de friedreich(harding, 1981).  hemos analizado las relaciones existentes entre las alteraciones cognitivas (exploracion neuropsicologica), la afectacion neurologica, el da\u00f1o estructural (resonancia magnetica nuclear, rm) y los parametros de neuroimagen funcional (spect), con el objetivo ultimo de aportar informacion al estudio de las funciones no-motoras del cerebelo.  los resultados de la exploracion neuropsicol\u00f3gica indican que los pacientes con ataxia de fiedrecich presentan alteraciones en las habilidades visocontructivas y visoperceptivas complejas, en memoria inmediata y capacidad de aprendizaje verbal y en fluidez verbal ante consignas foneticas, ademas de una elevada sensibilidad a la interferencia verbal proactiva. Estos deficits son indicativos de leve disfuncion fronto-temporo-parietal.  la valoracion cuantitativa de los estudios de rm muestra que, como grupo, los pacientes presentan degeracion cerebelosa y espinal, sin indicios de afectacion del puente cerebral, cuerpo calloso ni hemisferios cerebrales. en un analisis individualizado, observamos que un 67% de la muestra presenta atrofia cerebelosa (valores que se desvian en 2 de o mas del promedio del grupo de control).  los resultados de spect muestran dos patrones diferenciados de distribucion del flujo sanguineo cerebelo-cerebral: una baja perfusion cerebelosa se asocia a una relativamente alta perfusion frontal y una relativamente baja perfusion frontal y una alta perfusi\u00f3n temporo-occipital.  la integracion de los diferentes parametros estudiados nos permite concluir que existe una correspondencia anatomica y funcional: el patron de afectacion caracterizado por atrofia cerebelosa, hipoperfusion cerebelosa y temporo-occipital e hiperperfusion frontal esta r<\/p>\n<p>&nbsp;<\/p>\n<h3>Datos acad\u00e9micos de la tesis doctoral \u00ab<strong>Perfil neuropsicologico de las ataxias cerebelosas heredodegenerativas<\/strong>\u00ab<\/h3>\n<ul>\n<li><strong>T\u00edtulo de la tesis:<\/strong>\u00a0 Perfil neuropsicologico de las ataxias cerebelosas heredodegenerativas <\/li>\n<li><strong>Autor:<\/strong>\u00a0 Tone Wollmann Engeby <\/li>\n<li><strong>Universidad:<\/strong>\u00a0 La laguna<\/li>\n<li><strong>Fecha de lectura de la tesis:<\/strong>\u00a0 11\/05\/2001<\/li>\n<\/ul>\n<p>&nbsp;<\/p>\n<h3>Direcci\u00f3n y tribunal<\/h3>\n<ul>\n<li><strong>Director de la tesis<\/strong>\n<ul>\n<li>Jose Barroso Ribal<\/li>\n<\/ul>\n<\/li>\n<li><strong>Tribunal<\/strong>\n<ul>\n<li>Presidente del tribunal: Jos\u00e9 angel Berciano blanco <\/li>\n<li>isabel Portell cortes (vocal)<\/li>\n<li>sergio Hernadez exposito (vocal)<\/li>\n<li>Fernando Monton alvarez (vocal)<\/li>\n<\/ul>\n<\/li>\n<\/ul>\n<p>&nbsp;<\/p>\n","protected":false},"excerpt":{"rendered":"<p>Tesis doctoral de Tone Wollmann Engeby Este trabajo de investigaci\u00f3n valora el perfil neuropsicologico que caracteriza a una uestra de [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":0,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"site-sidebar-layout":"default","site-content-layout":"","ast-site-content-layout":"","site-content-style":"default","site-sidebar-style":"default","ast-global-header-display":"","ast-banner-title-visibility":"","ast-main-header-display":"","ast-hfb-above-header-display":"","ast-hfb-below-header-display":"","ast-hfb-mobile-header-display":"","site-post-title":"","ast-breadcrumbs-content":"","ast-featured-img":"","footer-sml-layout":"","theme-transparent-header-meta":"","adv-header-id-meta":"","stick-header-meta":"","header-above-stick-meta":"","header-main-stick-meta":"","header-below-stick-meta":"","astra-migrate-meta-layouts":"default","ast-page-background-enabled":"default","ast-page-background-meta":{"desktop":{"background-color":"var(--ast-global-color-4)","background-image":"","background-repeat":"repeat","background-position":"center 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